Enzyme Replacement Therapy

10 Drugs classified under this biological system

Enzyme Replacement Therapy. Laronidase 500 U / 5 ml.
VIAL: 1. See lit.
Long-term enzyme replace. ther. in
confirm. mucopolysaccharidos. I
(MPS I, alfa-I-iduronidase defic.) for nonneurolog. manifests. of the dis.

Enzyme Replacement Therapy. Imiglucerase 400 U/Vial.
VIAL (lyophilized pwdr. for infus.): 1.
See lit.
Long term enzyme replace. ther. in
confirmed diagn. type 1 Gaucher dis.

Alimentary tract and metabolism enzymes. Idursulfase 2 mg/ml.
VIAL (sol. for infus.): 1 x 3 ml. See lit.
Long-term tmt. Hunter Syndr. (MPS II).
C/I: Hypersens.

Enzymes. Taliglucerase Alfa 200 U/vial.
VIAL: 1× 200 U. The recomm. dosage for
tmt.-naïve adult &ped. pts. above 2 yrs.
of age and older is 60U/ kg of bdy. wt.
admin. every other wk. as a 60 to 120
min. IV. See lit.
Indic. for long-term enzyme replac. ther.
(ERT) for adult. & ped. pts. above 2 yrs.
with a confirm. diagnos. of Type 1
Gaucher dis.
C/I: Hypersens.

Enzyme Replacement Therapy. Agalsidase Beta 5 mg/ml, 35 mg/7ml.
PWDR. FOR INFUS: 1 x 5 mg/ml,
35 mg/ml. See lit.
Long-term enzyme replace. ther. in
confirmed diagnos. Fabry dis. (alfagalactosidase A defic.).

Enzyme Replacement Therapy. Velmanase alfa 10 mg/vial.
Pwder for sol. for infus.: 10 mg/vial.
Dose 1 mg/kg of BW admin. once / week by IV infus. at a contr. speed .
 Enzyme replac. ther. for the trt. of non-neurol. manifest. in pts. with mild to mod. alpha-mannosidosis
C/I:Hypersens.